Neurocognitive disorder due to prion disease

Neurocognitive Disorder due to Prion Disease". This disorder is rare but extremely devastating, as it is related to the accumulation of abnormal proteins in the brain. In this session, we will explore in detail this disease, its causes, symptoms, diagnosis, treatment and how to approach it from a leadership and support perspective.

Causes and Risk Factors

Abnormal Prion Proteins: These proteins become pathological and cause brain damage.

Genetic Variability: Some forms of prion disease are related to specific genetic mutations.

Types of Prion Diseases

Creutzfeldt-Jakob disease (CJD): The most common form of prion disease in humans and is characterized by rapid progression of neurological and cognitive symptoms.

Bovine Spongiform Encephalopathy (BSE): Also known as "mad cow" disease, it affects cattle and can sometimes be transmitted to humans.

Symptoms of Neurocognitive Disorder due to Prion Disease.

Cognitive Changes: Symptoms include memory impairment, abstract thinking problems, and difficulties in decision making.

Behavioral Changes: May include personality changes, apathy and neuropsychiatric symptoms.

Neurological Symptoms: Patients may experience problems with movement and coordination.

Diagnosis and Evaluation

Clinical Evaluation: Diagnosis is based on a comprehensive clinical evaluation that includes patient interviews, neurological testing, and laboratory testing.

Imaging Tests: Brain imaging, such as magnetic resonance imaging (MRI), may show characteristic changes in the brain.

Treatment and Management

Palliative Care: There is no cure for prion dis